Outcome of children with pulmonary lymphangiectasis.

Outcome of children with pulmonary lymphangiectasis.

Pediatr Pulmonol. 2009 Apr

Mettauer N, Agrawal S, Pierce C, Ashworth M, Petros A.

Paediatric Intensive Care Unit, Great Ormond Street Hospital for Children NHS Trust, London WC1N 3JH, United Kingdom. nmettauer@bluewin.ch

Pulmonary lymphangiectasis (PL) is a very rare developmental defect of the lungs, which has previously been reported to have a very poor prognosis. However, recent reports have suggested improved outcomes, possibly as a result of advances in neonatal and pediatric intensive care medicine. We performed a retrospective study on the outcome of children with PL between 1990 and 2008 referred to our tertiary center. Seven patients with histologically proven PL were identified over the 18-year period. Six patients presented in the neonatal period and one patient at 7 months of age, all of them requiring intensive care treatment. Three neonatal patients required extracorporeal membrane oxygenation (ECMO). Six of the seven patients did not survive including all those who received ECMO. Two of the six non-survivors died of other causes than their underlying disease. The only survivor had an antenatal diagnosis of hydrops and required in utero chest drain insertion. Postnatally he was managed with maximal medical treatment for bilateral pleural effusions and persistent pulmonary hypertension. A 7-month follow-up showed this infant to be doing well. In conclusion overall the prognosis of congenital PL remains poor. The one survivor demonstrates that this condition is survivable with aggressive intervention and as current evidence suggests gradual improvement of symptoms may occur over time, and that maximal medical treatment remains warranted. 

2009 Wiley-Liss, Inc.

Liquid Nitrogen Cryotherapy of Lymphangiectasia.

Liquid Nitrogen Cryotherapy of Lymphangiectasia.

Cornea. 2009 Apr 29

Fraunfelder FW.

From the Casey Eye Institute, Oregon Health & Science University, Portland, OR.

PURPOSE: To report a case of lymphangiectasia successfully treated with liquid nitrogen cryotherapy.

METHODS: A 1.5-mm Brymill cryoprobe (Brymill Cryogenic Systems, Ellington, CT) was applied in a double freeze-thaw method after an incisional biopsy of a portion of the conjunctiva. Freeze times were 1-2 seconds with thawing of 5-10 seconds between freezes.

RESULTS: A 64-year-old white man had symptoms of bilateral epiphora, eye irritation, and episodic blurred vision that was worse in the right eye. Ocular examination revealed inferior chemotic conjunctiva in the right eye and redundant conjunctiva in the left eye without chemosis. Marsupialization and liquid nitrogen cryotherapy were performed on the right eye, and the symptoms and signs resolved within 2 weeks. One year after cryotherapy, the patient has had no more eye symptoms or signs of lymphangiectasia.

CONCLUSION: Liquid nitrogen cryotherapy may be an effective alternative to surgery in the treatment of conjunctival lymphangiectasia.

PMID: 19421031 [PubMed - as supplied by publisher]

The efficacy of double balloon enteroscopy for patients with intestinal lymphangiectasia, case repor

The efficacy of double balloon enteroscopy for patients with intestinal lymphangiectasia, case report of primary intestinal lymphangiectasia.

Nippon Shokakibyo Gakkai Zasshi. 2008 Nov

Department of Gastroenterology, Graduate School of Medicine, Osaka City University.

A 31-year-old man has visited our hospital, complaining diarrhea and leg edema. Blood test showed hypoalbuminea, but we couldn't find the reason by several examinations. Therefore, we performed double balloon enteroscopy, and intestinal lymphangiectasia was diagnosed histologically by biopsy. It's useful and effective to perform double balloon enteroscopy and histological examination for the unknown origin case of protein loosing enteropathy.

J-Stage

PubMed - English

Magnetic resonance imaging as a new method to diagnose protein losing enteropathy

Magnetic resonance imaging as a new method to diagnose protein losing enteropathy

Lymphology. 2008 Sep

Department of Plastic & Reconstructive Surgery, Shanghai 9th People's Hospital, Shanghai Jiao Tong University School of Medicine, Shanghai, People's Republic of China.

The main cause of protein losing enteropathy (PLE) in children is intestinal lymphangiectasia. PLE is commonly diagnosed with radiotracer scintigraphy. We report the use of magnetic resonant imaging in diagnosis of a child with primary PLE. MRI clearly revealed abnormality in intestine and mesentery and dilated thoracic duct and mesenteric lymphatic as well as prominent subcutaneous lymphatics in the extremity. We conclude that MRI is a useful tool in diagnose of primary PLE.

PMID: 19013878 [PubMed - in process]

Pat O'Connor Medical Blogs and Online Support Groups

Good Morning Everyone

Many of you know I have a few medical blogs and support groups - and
there have been significant changes. AOL wiped out all their groups
and blogs, so I had to move everything from there to another place.

Sooooooooo......here is an updated list for all my medical blogs and
support groups.

Pat

***My Lymphedema, Lymphatic, Edema, Medical Blogs***

My Life with Lymphedema

Frontline personal blog on lymphedema which includes many
inspirational articles and writings as well. Find information,
support and most importantly hope. Life is not a requiem for that
which we can not do, but a celebration for that which we can.

http://mylifewithlymphedema.blogspot.com/

Developmental Disorders of the Lymphatics

Information and resources for medical conditions relating to the
developement of the lymphatic system. Clearing house for peer
reviewed information and news. Includes all disorders of lymphatic
dysplasia

http://lymphsystemdisorders.blogspot.com

Edema and Related Medical Conditions

Clearinghouse for peer reviewed information and articles relating to
edema (swelling) related medical conditions. Includes conditions,
causes and treatments

http://edemainformation.blogspot.com/

Lymphedemaville

This is about journeying through life with a medical condition called
lymphedema. ... What it is, what it is like, what to expect , how to
treat the condition, and most important discovering hope in having a
rich and wonderful life despite lymphedema.

http://lymphedemaville.wordpress.com/

Disorders of the Lymph System

Peer reviewed information on disorders relating to the lymph system,
lymph nodes and lymph vessels.

http://lymphaticdisorders.wordpress.com/

Bacterial Infections

Information on all types of bacterial infections. Peer reviewed new
and information on causes, prevention and treatments.

http://bacteriainfections.blogspot.com

Antibiotics

Complete guide to antibiotics. Clearinghouse of peer reviewed
information on what antibiotics do, what they treat and how they work
and most importantly when or when not to use them.

http://antibioticinformation.blogspot.com/

Fungal Infections

Clearinghouse of peer reviewed news and information on all types of
fungal infections. Causes, Symptoms, Treatments and Prevention are
covered.

http://fungalinfections.wordpress.com/

Cellulitis

Clearinghouse for the infection known as cellulitis. Peer reviewed
news and information on its causes, treatments, prevention and
complications

http://cellulitisinfections.blogspot.com/

Trisomy Disorders

Peer reviewed information on chromosome disorders. These include Down
Syndrome, Turner Syndrome, Klinefelter Syndrome, Prader-Willi
syndrome, 22q11 deletion syndrome, Cri-du-chat (cat cry) syndrome,
Turner's Syndrome and more.

http://trisomydisorders.wordpress.com/

Lipedema

Millions of people are afflicted with this almost totally
misunderstood and frustrating medical condition. Articles relating to
living with lipedema, treatments and other peeer reviewed
information. Works in conjunction with our online support group
Lipedema

http://www.xanga.com/lipedema

Lymphangiectasia/Xanga

Medical condition caused by the dilation of the lymphatic vessels.
Peer reviewed medical information and news with personal stories
about how patients can cope with this little understood condition.
Works inconjunction with our online support group All About
Lymphangiectasia

http://www.xanga.com/lymphangiectasia

Lymphangiectasia

Medical condition caused by the dilation of the lymphatic vessels.
Peer reviewed medical information and news with personal stories
about how patients can cope with this little understood condition.
Works inconjunction with our online support group All About
Lymphangiectasia

http://lymphangiectasia.blogspot.com/

Lymphedema

Another one of our blogs on the medical condition lymphedema. Peer
reviewed information on causes, treatments complications and personal
accounts of coping with lymphedema

http://www.xanga.com/lymphedema

Lymphedema

Another one of our blogs on the medical condition lymphedema. Peer
reviewed information on causes, treatments, complications and
personal articles on coping with this little understood noncurable
condition

http://lymphedemahome.livejournal.com/

MRSA Information

Peer reviewed information on the causes, treatments, complications
and prevention of this emerging and potentially deadly spreading
infection

http://mrsainformation.blogspot.com/

Men's Health - Xanga

Articles and information relating to a broad spectrum of medical and
health issues relating to men.

http://www.xanga.com/Mens_Health

Alternative Medicine and Lymphedema

In this blog, we will explore all the various alternative medicine
treatments used or proposed for lymphedema and whether or not they
are both effective and save.

http://alternativemedicinelymphedema.blog.com/

Cutaneous Lymphoma

As a thirteen year survivor of lymphoma, this is of special interest
to me. This is a cancer that is increasing in the numbers afflicted
with it and until recently not well understood. Peer reviewed
information on symptoms, diagnosis, treatments and compInformation
and resources for medical conditions relating to the developement of
the lymphatic system. Clearing house for peer reviewed information
and news

http://cutaneouslymphoma.blogspot.com/

Kaposi's Sarcoma

A rapidly emerging form of cancer. Clearinghouse of peer reviewed
information on causes, symptoms, treatments, diagnosis and
complications.

http://kaposissarcomainfo.blogspot.com/

Merkel Cell Cancer

Clearinghouse of peer reviewed information on this emerging and
rapididly increasing form of cancer. Diagnosis, Treatments,
Management and complications

http://merkelcellcancer.blogspot.com/

Lymphedema of the Leg

http://lymphedemaoftheleg.blogspot.com/

Burkitt's Lymphoma

This information is about specific types of non-Hodgkin lymphoma
known as Burkitt lymphoma and Burkitt-like lymphoma.

http://burkittslymphoma.blog.com/

***Our Family of On Line Support Groups***

Advocates for Lymphedema

Our frontline online support group for lymphedema.  Provides community, support, information and advocacy on behalf of patients from all corners of the globe.

http://health.groups.yahoo.com/group/AdvocatesforLymphedema/

Children with Lymphedema

A very special support group for children who have lymphedema and their parents.  Tremendous source of community, support and information on the day to day care of children with the condition.

http://health.groups.yahoo.com/group/childrenwithlymphedema/

Men with Lymphedema

Support group for men who have lymphedema.  Brotherhood, comradere, support and information - a safe place to let the hair down and ask questions and interact.

http://health.groups.yahoo.com/group/menwithlymphedema/

Teens with Lymphedema

A special group for teenagers who face difficult issues during their teen years in how to cope with, live with and most important to learn how to live a rich and rewarding life despite having lymphedema

 http://health.groups.yahoo.com/group/Teens_with_Lymphedema/

All About Lymphangiectasia

Support group for parents, patients, children who suffer from all forms of lymphangiectasia. This condition is caused by dilation of the lymphatics. It can affect the intestinal tract, lungs and other critical body areas. Works inconjunction with our Xanga blog Lymphangiectasia 

http://health.groups.yahoo.com/group/allaboutlymphangiectasia/

Lipedema, Lipodema, Lipoedema

Millions of people are afflicted with this almost totally misunderstood and frustrating medical condition.  Articles relating to living with lipedema, treatments and other peeer reviewed information. Works in conjunction with our online support group Lipedema

 http://health.groups.yahoo.com/group/lipedema_lipodema_lipoedema/                     

Lymphatic Disorders Support Group

Works in conjunction with our blogs on Disorders of the Lymph System and Developemental Disorders of the lymph system.  All lymphatic conditions included with special emphasis on lymphatic malformations, lymphangiomas, cystic hygromas, Castleman's Disease

 http://health.groups.yahoo.com/group/lymphaticdisorders/

All About Lymphoedema – Australia

Support group for our friends down under with lymphedema.  Provides a great sources of information, community and support.

http://au.groups.yahoo.com/group/All_About_Lymphoedema/

All About Lymphedema

Our frontline Google support group for lymphedema.  Information, support, community and help.

http://groups-beta.google.com/group/All-About-Lymphedema

Lymphedema Research

A leader in providing peer reviewed research studies and abstracts on lymphedema.

http://groups.google.com/group/lymphedemaresearch